ETHE1 anticorps

N° du produit ABIN7255167

Détail du produit anti-ETHE1 anticorps

Antigène: ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp ETHE1 est non-conjugé

Application: Western Blotting (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)

Attributs du produit: Polyclonal Antibody

Purification: Affinity purification

Immunogène: Recombinant fusion protein of human ETHE1 (NP_055112.2).

Isotype: IgG

Information d'application

Indications d'application: WB 1:200-1:1000 IHC 1:50-1:200 IF 1:50-1:200

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur ETHE1

Antigène: ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))

Autre désignation: ETHE1 (ETHE1 Produits)

Synonymes: anticorps zgc:85680, anticorps HSCO, anticorps YF13H12, anticorps 0610025L15Rik, anticorps Hsco, anticorps ETHE1, persulfide dioxygenase, anticorps ethylmalonic encephalopathy 1, anticorps Ethe1, anticorps ethe1, anticorps ETHE1

Sujet: This gene encodes a member of the metallo beta-lactamase family of iron-containing proteins involved in the mitochondrial sulfide oxidation pathway. The encoded protein catalyzes the oxidation of a persulfide substrate to sulfite. Certain mutations in this gene cause ethylmalonic encephalopathy, an infantile metabolic disorder affecting the brain, gastrointestinal tract and peripheral vessels. Alternative splicing results in multiple transcript variants encoding different isoforms.

Poids moléculaire:

Observed_MW: 28 kDa

Calculated_MW: 27 kDa

ID gène: 23474

UniProt: O95571