Dystrophin anticorps

N° du produit ABIN7008615

Détail du produit anti-Dystrophin anticorps

Antigène: Dystrophin (DMD)

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp Dystrophin est non-conjugé

Application: Western Blotting (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)

Attributs du produit: Polyclonal Antibody

Purification: Affinity purification

Immunogène: Recombinant fusion protein of human DMD (NP_004007.1).

Isotype: IgG

Information d'application

Indications d'application: WB 1:200-1:2000 IHC 1:50-1:200 IF 1:50-1:200

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur Dystrophin

Antigène: Dystrophin (DMD)

Autre désignation: DMD (DMD Produits)

Synonymes: anticorps DMD, anticorps Dmd, anticorps MGC83347, anticorps DKFZp459C1629, anticorps dmd, anticorps MGC79631, anticorps DKFZp468A1620, anticorps Dp71, anticorps cb664, anticorps zfDYS, anticorps im:6911785, anticorps zgc:110165, anticorps BMD, anticorps CMD3B, anticorps DXS142, anticorps DXS164, anticorps DXS206, anticorps DXS230, anticorps DXS239, anticorps DXS268, anticorps DXS269, anticorps DXS270, anticorps DXS272, anticorps DXSmh7, anticorps DXSmh9, anticorps Dp427, anticorps dys, anticorps mdx, anticorps pke, anticorps DNADMD1, anticorps RATDMD, anticorps CG17750, anticorps CG31175, anticorps CG34157, anticorps CG7240, anticorps CG7243, anticorps CG7344, anticorps DLP, anticorps DLP1, anticorps DLP186, anticorps DLP2, anticorps DLP3, anticorps DmDLP, anticorps DmDYS, anticorps Dmel\\CG34157, anticorps Dp117, anticorps Dp186, anticorps Dp205, anticorps GI3046716, anticorps IDLP, anticorps det, anticorps dmDLP, anticorps dmDp186, anticorps dmDys, anticorps dystrophin, anticorps dystrophin, gene 1 L homeolog, anticorps dystrophin, gene 1, anticorps dystrophin, muscular dystrophy, anticorps Dystrophin, anticorps DMD, anticorps LOC708073, anticorps dmd.1.L, anticorps LOC465557, anticorps dmd.1, anticorps dmd, anticorps Dmd, anticorps Dys

Sujet: This gene spans a genomic range of greater than 2 Mb and encodes a large protein containing an N-terminal actin-binding domain and multiple spectrin repeats. The encoded protein forms a component of the dystrophin-glycoprotein complex (DGC), which bridges the inner cytoskeleton and the extracellular matrix. Deletions, duplications, and point mutations at this gene locus may cause Duchenne muscular dystrophy (DMD), Becker muscular dystrophy (BMD), or cardiomyopathy. Alternative promoter usage and alternative splicing result in numerous distinct transcript variants and protein isoforms for this gene.

Poids moléculaire:

Observed_MW: 427 kDa

Calculated_MW: 57-72 kDa/271 kDa/425-426 kDa

ID gène: 1756

UniProt: P11532

Pathways: Skeletal Muscle Fiber Development