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Dysferlin anticorps

Cet anticorps Lapin Polyclonal détecte spécifiquement Dysferlin dans WB et ELISA. Il présente une réactivité envers Humain.
N° du produit ABIN7181039

Aperçu rapide pour Dysferlin anticorps (ABIN7181039)

Antigène

Voir toutes Dysferlin (DYSF) Anticorps
Dysferlin (DYSF)

Reactivité

  • 57
  • 24
  • 5
  • 4
  • 4
  • 4
  • 4
  • 2
  • 2
  • 2
  • 2
Humain

Hôte

  • 51
  • 5
  • 1
Lapin

Clonalité

  • 43
  • 14
Polyclonal

Conjugué

  • 24
  • 4
  • 3
  • 2
  • 2
  • 2
  • 2
  • 2
  • 2
  • 2
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
Cet anticorp Dysferlin est non-conjugé

Application

  • 18
  • 15
  • 14
  • 14
  • 7
  • 6
  • 4
  • 2
  • 2
  • 1
  • 1
Western Blotting (WB), ELISA
  • Fonction

    DYSF Antibody

     Réactivité croisée

    Souris

    Purification

    The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.

    Immunogène

    Synthesized peptide derived from Human Dysferlin.

    Isotype

    IgG
  • Indications d'application

    Optimal working dilution should be determined by the investigator.

    Restrictions

    For Research Use only
  • Format

    Liquid

    Buffer

    phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150 mM NaCl, 0.02 % sodium azide and 50 % glycerol.

    Agent conservateur

    Sodium azide

    Précaution d'utilisation

    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

    Stock

    -20 °C,-80 °C

    Stockage commentaire

    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • Antigène

    Dysferlin (DYSF)

    Autre désignation

    DYSF

    Sujet

    Background: Key calcium ion sensor involved in the Ca2+-triggered synaptic vesicle-plasma membrane fusion. Plays a role in the sarcolemma repair mechanism of both skeletal muscle and cardiomyocytes that permits rapid resealing of membranes disrupted by mechanical stress By similarity.

    Delia J. Hern?ez-Deviez, Hum. Mol. Genet., Jan 2006, 15: 129 - 142.
    Yanchao Huang, FASEB J, Mar 2007, 21: 732 - 742.
    Mengfatt Ho, Hum. Mol. Genet., Sep 2004, 13: 1999 - 2010.
    Eriko Fujita, Hum. Mol. Genet., Mar 2007, 16: 618 - 629.

    Aliases: DMAT antibody, DYSF antibody, DYSF_HUMAN antibody, Dysferlin antibody, Dysferlin limb girdle muscular dystrophy 2B (autosomal recessive) antibody, Dysferlin limb girdle muscular dystrophy 2B antibody, Dystrophy associated fer 1 like 1 antibody, Dystrophy associated fer 1 like protein antibody, Dystrophy associated fer1 like 1 antibody, Dystrophy associated fer1 like protein antibody, Dystrophy-associated fer-1-like protein antibody, Fer 1 like protein 1 antibody, Fer-1-like protein 1 antibody, Fer1 like protein 1 antibody, FER1L1 antibody, FLJ00175 antibody, FLJ90168 antibody, LGMD 2B antibody, LGMD2B antibody, Limb girdle muscular dystrophy 2B (autosomal recessive) antibody, Limb girdle muscular dystrophy 2B antibody, Miyoshi myopathy antibody, MM antibody, MMD1 antibody

    UniProt

    O75923
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