Dysferlin anticorps
Aperçu rapide pour Dysferlin anticorps (ABIN7181039)
Antigène
Voir toutes Dysferlin (DYSF) AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
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Fonction
- DYSF Antibody
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Réactivité croisée
- Souris
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Purification
- The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
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Immunogène
- Synthesized peptide derived from Human Dysferlin.
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Isotype
- IgG
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Indications d'application
- Optimal working dilution should be determined by the investigator.
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Restrictions
- For Research Use only
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Format
- Liquid
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Buffer
- phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150 mM NaCl, 0.02 % sodium azide and 50 % glycerol.
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Stock
- -20 °C,-80 °C
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Stockage commentaire
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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- Dysferlin (DYSF)
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Autre désignation
- DYSF
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Sujet
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Background: Key calcium ion sensor involved in the Ca2+-triggered synaptic vesicle-plasma membrane fusion. Plays a role in the sarcolemma repair mechanism of both skeletal muscle and cardiomyocytes that permits rapid resealing of membranes disrupted by mechanical stress By similarity.
Delia J. Hern?ez-Deviez, Hum. Mol. Genet., Jan 2006, 15: 129 - 142.
Yanchao Huang, FASEB J, Mar 2007, 21: 732 - 742.
Mengfatt Ho, Hum. Mol. Genet., Sep 2004, 13: 1999 - 2010.
Eriko Fujita, Hum. Mol. Genet., Mar 2007, 16: 618 - 629.Aliases: DMAT antibody, DYSF antibody, DYSF_HUMAN antibody, Dysferlin antibody, Dysferlin limb girdle muscular dystrophy 2B (autosomal recessive) antibody, Dysferlin limb girdle muscular dystrophy 2B antibody, Dystrophy associated fer 1 like 1 antibody, Dystrophy associated fer 1 like protein antibody, Dystrophy associated fer1 like 1 antibody, Dystrophy associated fer1 like protein antibody, Dystrophy-associated fer-1-like protein antibody, Fer 1 like protein 1 antibody, Fer-1-like protein 1 antibody, Fer1 like protein 1 antibody, FER1L1 antibody, FLJ00175 antibody, FLJ90168 antibody, LGMD 2B antibody, LGMD2B antibody, Limb girdle muscular dystrophy 2B (autosomal recessive) antibody, Limb girdle muscular dystrophy 2B antibody, Miyoshi myopathy antibody, MM antibody, MMD1 antibody
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UniProt
- O75923
Antigène
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