IDUA anticorps (AA 28-634)

N° du produit ABIN7873280

Cet anticorps Lapin Polyclonal détecte spécifiquement IDUA dans ELISA, WB, FACS, IHC (p) et IF. Il présente une réactivité avec des échantillons de Humain, Souris et Rat.

Aperçu rapide pour IDUA anticorps (AA 28-634) (ABIN7873280)

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp IDUA est non-conjugé

Application: ELISA, Western Blotting (WB), Flow Cytometry (FACS), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Immunofluorescence (IF)

Détail du produit anti-IDUA anticorps

Épitope: AA 28-634

Fonction: IDUA Antibody / Alpha-L-iduronidase

Purification: Antigen affinity purified

Immunogène: An E.coli-derived human recombinant protein (amino acids A28-D634) was used as the immunogen for the IDUA antibody.

Isotype: IgG

Information d'application

Indications d'application: Optimal dilution of the IDUA antibody should be determined by the researcher.

Restrictions: For Research Use only

Stockage

Format: Lyophilized

Buffer: 0.5 mg/mL if reconstituted with 0.2 mL sterile DI water

Stock: 4 °C,-20 °C

Stockage commentaire: After reconstitution, the IDUA antibody can be stored for up to one month at 4oC. For long-term, aliquot and store at -20oC. Avoid repeated freezing and thawing.

Détails sur IDUA

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Autre désignation: IDUA

Sujet: This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).

UniProt: P35475

Pathways: Glycosaminoglycan Metabolic Process