GLA anticorps (AA 83-112)

N° du produit ABIN7876930

Cet anticorps anti-GLA Polyclonal Lapin (ABIN7876930) détecte spécifiquement GLA dans WB, FACS, IF et IHC (p). L’anticorps est réactif avec des échantillons de Humain.

Aperçu rapide pour GLA anticorps (AA 83-112) (ABIN7876930)

Antigène: GLA (Galactosidase, alpha (GLA))

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp GLA est non-conjugé

Application: Western Blotting (WB), Flow Cytometry (FACS), Immunofluorescence (IF), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))

Détail du produit anti-GLA anticorps

Épitope: AA 83-112

Fonction: Galactosidase alpha Antibody / Gla

Purification: Purified

Immunogène: A portion of amino acids 83-112 from the human protein was used as the immunogen for the Galactosidase alpha antibody.

Isotype: Ig Fraction

Information d'application

Indications d'application: The stated application concentrations are suggested starting points. Titration of the Galactosidase alpha antibody may be required due to differences in protocols and secondary/substrate sensitivity.

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: In 1X PBS, pH 7.4, with 0.09 % sodium azide

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Aliquot the Galactosidase alpha antibody and store frozen at -20oC or colder. Avoid repeated freeze-thaw cycles.

Détails sur GLA

Antigène: GLA (Galactosidase, alpha (GLA))

Autre désignation: Galactosidase alpha

Sujet: GLA is a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.

UniProt: P06280

Pathways: SARS-CoV-2 Protein Interactome