GLA anticorps
Aperçu rapide pour GLA anticorps (ABIN7880847)
Antigène
Voir toutes GLA AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
-
-
Fonction
- Galactosidase alpha Antibody / Gla
-
Séquence
- KRKLGFYEWT SRLRSHIN
-
Purification
- Affinity purified
-
Immunogène
- Amino acids KRKLGFYEWTSRLRSHIN from the human protein were used as the immunogen for the Galactosidase alpha antibody.
-
Isotype
- IgG
-
-
-
-
Indications d'application
- Optimal dilution of the Galactosidase alpha antibody should be determined by the researcher.
-
Restrictions
- For Research Use only
-
-
-
Format
- Lyophilized
-
Buffer
- 0.5 mg/mL if reconstituted with 0.2 mL sterile DI water
-
Stock
- 4 °C,-20 °C
-
Stockage commentaire
- After reconstitution, the Galactosidase alpha antibody can be stored for up to one month at 4oC. For long-term, aliquot and store at -20oC. Avoid repeated freezing and thawing.
-
-
- GLA (Galactosidase, alpha (GLA))
-
Autre désignation
- Galactosidase alpha
-
Sujet
- Alpha-galactosidase is a glycoside hydrolase enzyme that encoded by the GLA gene. This gene is a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.
-
UniProt
- P06280
-
Pathways
- SARS-CoV-2 Protein Interactome
Antigène
-