IDUA anticorps (AA 1-87) (Fluoro550)

N° du produit ABIN7999063

L’anticorps anti-IDUA Polyclonal Lapin est utilisé pour la détection de IDUA dans des échantillons de Humain, Souris et Rat. Il a été validé pour FACS.

Aperçu rapide pour IDUA anticorps (AA 1-87) (Fluoro550) (ABIN7999063)

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp IDUA est conjugé à/à la Fluoro550

Application: Flow Cytometry (FACS)

Détail du produit anti-IDUA anticorps (Fluoro550)

Épitope: AA 1-87

Fonction: Anti-IDUA Antibody Fluoro550 Conjugated

Réactivité croisée (Details): No cross reactivity with other proteins.

Purification: Immunogen affinity purified.

Immunogène: E.coli-derived human INSIG1 recombinant protein (Position: M1-R87).

Isotype: IgG

Information d'application

Indications d'application: Flow Cytometry, Optimal dilutions should be determined by end users.

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: Each vial contains 50 % glycerol, 0.9 % NaCl, 0.2 % Na2HPO4, 0.02 % Sodium azide.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: At -20°C for one year from date of receipt. Avoid repeated freezing and thawing. Protect from light.

Date de péremption: 12 months

Détails sur IDUA

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Autre désignation: IDUA

Sujet:

Background: This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).

Gene Full Name: alpha-L-iduronidase

ID gène: 3425

UniProt: P35475

Pathways: Glycosaminoglycan Metabolic Process