ALAD anticorps (AA 151-240) (FITC)

N° du produit ABIN882123

Détail du produit anti-ALAD anticorps (FITC)

Antigène: ALAD (Aminolevulinate Dehydratase (ALAD))

Épitope: AA 151-240

Reactivité: Souris

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp ALAD est conjugé à/à la FITC

Application: Western Blotting (WB), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))

Réactivité croisée: Souris

Homologie: Human,Rat,Dog,Cow,Sheep,Horse,Rabbit

Purification: Purified by Protein A.

Immunogène: KLH conjugated synthetic peptide derived from human ALAD

Isotype: IgG

Information d'application

Indications d'application: IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 μg/μL

Buffer: Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.

Agent conservateur: ProClin

Précaution d'utilisation: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

Date de péremption: 12 months

Détails sur ALAD

Antigène: ALAD (Aminolevulinate Dehydratase (ALAD))

Autre désignation: ALAD (ALAD Produits)

Synonymes: anticorps DDBDRAFT_0190269, anticorps DDBDRAFT_0231415, anticorps DDB_0190269, anticorps DDB_0231415, anticorps ALAD, anticorps ncf, anticorps ALADH, anticorps PBGS, anticorps ALADR, anticorps aminolevulinatedelta-dehydratase, anticorps zgc:110219, anticorps Lv, anticorps delta-aminolevulinate dehydratase, anticorps aminolevulinate dehydratase, anticorps delta-aminolevulinic acid dehydratase, anticorps Delta-aminolevulinic acid dehydratase, anticorps aminolevulinate dehydratase L homeolog, anticorps aminolevulinate, delta-, dehydratase, anticorps hemB, anticorps ALAD, anticorps PBGS, anticorps STY0404, anticorps SAS1597, anticorps SACI_RS03725, anticorps PAAG_00299, anticorps VDBG_00315, anticorps HPPC_00830, anticorps MGYG_01952, anticorps hem2, anticorps alad.L, anticorps Alad, anticorps alad

Sujet:

Synonyms: ALAD, ALADH, ALADR, Aminolevulinate dehydratase, Aminolevulinate, delta, dehydratase, Delta aminolevulinic acid dehydratase, Delta-aminolevulinic acid dehydratase, HEM2_HUMAN, Lv, PBGS, Porphobilinogen synthase.

Background: Catalyzes an early step in the biosynthesis of tetrapyrroles. Binds two molecules of 5-aminolevulinate per subunit, each at a distinct site, and catalyzes their condensation to form porphobilinogen.Involvement in disease:Defects in ALAD are the cause of acute hepatic porphyria (AHP). AHP is a form of porphyria. Porphyrias are inherited defects in the biosynthesis of heme, resulting in the accumulation and increased excretion of porphyrins or porphyrin precursors. They are classified as erythropoietic or hepatic, depending on whether the enzyme deficiency occurs in red blood cells or in the liver. AHP is characterized by attacks of gastrointestinal disturbances, abdominal colic, paralysis, and peripheral neuropathy. Most attacks are precipitated by drugs, alcohol, caloric deprivation, infections, or endocrine factors.

ID gène: 210

UniProt: P13716