Hexosaminidase A anticorps (C-Term)

N° du produit ABIN926663

L’anticorps Lapin Polyclonal anti-Hexosaminidase A a été validé pour WB. Il convient pour détecter Hexosaminidase A dans des échantillons de Humain.

Aperçu rapide pour Hexosaminidase A anticorps (C-Term) (ABIN926663)

Antigène: Hexosaminidase A (HEXA)

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp Hexosaminidase A est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-Hexosaminidase A anticorps

Épitope: C-Term

Purification: Purified

Immunogène: HEXA antibody was raised in rabbit using the C terminal of HEXA as the immunogen

Information d'application

Indications d'application: Optimal conditions should be determined by the investigator.

Commentaires:

HEXA Blocking Peptide, (ABIN5613994), is also available for use as a blocking control in assays to test for specificity of this HEXA antibody

Restrictions: For Research Use only

Stockage

Format: Lyophilized

Concentration: Lot specific

Buffer: Lyophilized powder. Add 50 µL of distilled water. Final antibody concentration is 1 mg/mL in PBS buffer.

Conseil sur la manipulation: Avoid repeated freeze/thaw cycles.

Stock: 4 °C/-20 °C

Stockage commentaire: Store at 4 °C, following reconstitution, aliquot and store at -20 °C.

Détails sur Hexosaminidase A

Antigène: Hexosaminidase A (HEXA)

Autre désignation: HEXA

Sujet: This gene encodes the alpha subunit of the lysosomal enzyme beta-hexosaminidase that, together with the cofactor GM2 activator protein, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Beta-hexosaminidase is composed of two subunits, alpha and beta, which are encoded by separate genes. Both beta-hexosaminidase alpha and beta subunits are members of family 20 of glycosyl hydrolases. Mutations in the alpha or beta subunit genes lead to an accumulation of GM2 ganglioside in neurons and neurodegenerative disorders termed the GM2 gangliosidoses. Alpha subunit gene mutations lead to Tay-Sachs disease (GM2-gangliosidosis type I). Synonyms: Polyclonal HEXA antibody, Anti-HEXA antibody, hexosaminidase A, alpha polypeptide antibody, MGC99608 antibody, TSD antibody.

Pathways: Sensory Perception of Sound, Glycosaminoglycan Metabolic Process