PEX19 anticorps (C-Term)

N° du produit ABIN926758

Cet anticorps Lapin Polyclonal détecte spécifiquement PEX19 dans WB. Il présente une réactivité avec des échantillons de Humain.

Aperçu rapide pour PEX19 anticorps (C-Term) (ABIN926758)

Antigène: PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp PEX19 est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-PEX19 anticorps

Épitope: C-Term

Purification: Purified

Immunogène: PEX19 antibody was raised in rabbit using the C terminal of PEX19 as the immunogen

Information d'application

Indications d'application: Optimal conditions should be determined by the investigator.

Commentaires:

PEX19 Blocking Peptide, (ABIN936282), is also available for use as a blocking control in assays to test for specificity of this PEX19 antibody

Restrictions: For Research Use only

Stockage

Format: Lyophilized

Concentration: Lot specific

Buffer: Lyophilized powder. Add 50 µL of distilled water. Final antibody concentration is 1 mg/mL in PBS buffer.

Conseil sur la manipulation: Avoid repeated freeze/thaw cycles.

Stock: 4 °C/-20 °C

Stockage commentaire: Store at 4 °C, following reconstitution, aliquot and store at -20 °C.

Détails sur PEX19

Antigène: PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))

Autre désignation: PEX19

Sujet: This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is also known as PBD-CGJ. Alternative splicing results in multiple transcript variants. Synonyms: Polyclonal PEX19 antibody, Anti-PEX19 antibody, peroxisomal biogenesis factor 19 antibody, D1S2223E antibody, FLJ55296 antibody, HK33 antibody, PMP1 antibody, PMPI antibody, PXF antibody, PXMP1 antibody.