AGLU anticorps (N-Term)

N° du produit ABIN950380

Cet anticorps Lapin Polyclonal détecte spécifiquement AGLU dans WB, EIA et IHC (p). Il présente une réactivité envers Humain.

Aperçu rapide pour AGLU anticorps (N-Term) (ABIN950380)

Antigène: AGLU (alpha-Glucosidase (AGLU))

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp AGLU est non-conjugé

Application: Western Blotting (WB), Enzyme Immunoassay (EIA), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))

Détail du produit anti-AGLU anticorps

Épitope: AA 173-203, N-Term

Specificité: This antibody recognizes Human Alpha-glucosidase (N-term).

Purification: Protein A column, followed by peptide affinity purification

Immunogène: conjugated synthetic peptide between 173-203 amino acids from the N-terminal region of Human Alpha-glucosidase Genename: GAA

Isotype: Ig Fraction

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.25 mg/mL

Buffer: PBS containing 0.09 % (W/V) Sodium Azide as preservative

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeated freezing and thawing.

Stock: 4 °C/-20 °C

Stockage commentaire: Store undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.

Détails sur AGLU

Antigène: AGLU (alpha-Glucosidase (AGLU))

Autre désignation: alpha-Glucosidase

Sujet: This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.Synonyms: Acid maltase, Aglucosidase alfa, GAA, LYAG, Lysosomal alpha-glucosidase

Poids moléculaire: 105319 Da

ID gène: 2548

NCBI Accession: NP_000143

Pathways: Cellular Glucan Metabolic Process