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DBT Produits

(Dihydrolipoamide Branched Chain Transacylase E2 (DBT))

Catégories

The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined. [provided by RefSeq, Jul 2008].

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Catégories DBT en vedette

DBT Anticorps

High quality antibodies with extensive validation data.

DBT Kits ELISA

Reliable ELISA kits for a wide range of species.

DBT Protéines

Proteins for various applications incl. WB, ELISA, IF etc.

DBT recommandé Anticorps

Produit
Reactivity
Application
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Application WB
Validations
  • (1)
  • (3)
N° du produit ABIN514887
Quantité 50 μg
Fiche technique Fiche technique
Reactivity Bat, Cow, Dog, Guinea Pig, Horse, Human, Monkey, Mouse, Pig, Rabbit, Rat
Application WB, IHC, IHC (p)
Validations
  • (4)
N° du produit ABIN6745750
Quantité 100 μL
Fiche technique Fiche technique
Reactivity Human
Application WB
Validations
  • (3)
N° du produit ABIN947782
Quantité 100 μg
Fiche technique Fiche technique

DBT recommandé Kits ELISA

Produit
Reactivity
Analytical Method
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
N° du produit ABIN6966364
Quantité 96 tests
Fiche technique Fiche technique
Reactivity Human
Analytical Method
Validations
N° du produit ABIN1140790
Quantité 96 tests
Fiche technique Fiche technique
Reactivity Cow
Analytical Method
Validations
N° du produit ABIN1140789
Quantité 96 tests
Fiche technique Fiche technique

DBT recommandé Protéines

Produit
Reactivity
Source
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
N° du produit ABIN3084921
Quantité 1 mg
Fiche technique Fiche technique
Reactivity Mouse
Source Escherichia coli (E. coli)
Validations
  • (1)
N° du produit ABIN3134462
Quantité 1 mg
Fiche technique Fiche technique
Reactivity Human
Source HEK-293 Cells
Validations
  • (1)
N° du produit ABIN2719240
Quantité 20 μg
Fiche technique Fiche technique

Dernières publications sur nos produits DBT

Johnson, Vidoni, Durigon, Pearce, Rorbach, He, Brea-Calvo, Minczuk, Reyes, Holt, Spinazzola: "Amino acid starvation has opposite effects on mitochondrial and cytosolic protein synthesis." dans: PLoS ONE, Vol. 9, Issue 4, pp. e93597, (2014) (PubMed).

Fredersdorf, Milne, Hall, Lu: "Characterization of a panel of novel anti-p21Waf1/Cip1 monoclonal antibodies and immunochemical analysis of p21Waf1/Cip1 expression in normal human tissues." dans: The American journal of pathology, Vol. 148, Issue 3, pp. 825-35, (1997) (PubMed).

Levine: "p53, the cellular gatekeeper for growth and division." dans: Cell, Vol. 88, Issue 3, pp. 323-31, (1997) (PubMed).

Synonymes et noms alternatifs relatifs à DBT

dihydrolipoamide branched chain transacylase E2 (DBT), dihydrolipoamide branched chain transacylase E2 (dbt), dihydrolipoamide branched chain transacylase E2 (CpipJ_CPIJ006326), dihydrolipoamide branched chain transacylase E2 (BDBG_05874), dihydrolipoamide branched chain transacylase E2 (NAEGRDRAFT_78509), dihydrolipoamide branched chain transacylase E2 (VDBG_04820), hypothetical protein (PGTG_17722), dihydrolipoamide branched chain transacylase E2 (Dbt), dihydrolipoamide branched chain transacylase E2 L homeolog (dbt.L), BCATE2, BCKAD-E2, BCKADE2, D3Wsu60e, E2, E2B, E2b, im:7147214, zgc:103768

Protein level used designations for DBT

  • lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
  • dihydrolipoamide branched chain transacylase E2
  • BCKAD E2 subunit
  • E2 component of branched chain alpha-keto acid dehydrogenase complex
  • branched chain acyltransferase, E2 component
  • branched-chain alpha-keto acid dehydrogenase complex component E2
  • dihydrolipoamide acetyltransferase component of branched-chain alpha-keto acid dehydrogenase complex
  • dihydrolipoyl transacylase
  • dihydrolipoyllysine-residue (2-methylpropanoyl)transferase
  • lipoamide acyltransferase component of mitochondrial branched-chain alpha-keto acid dehydrogenase complex
  • mitochondrial branched chain alpha-keto acid dehydrogenase transacylase subunit (E2b)
  • BCKAD E2
  • BCKAD-E2
  • BCKADE2
  • branched-chain alpha-ketoacid dehydrogenase, E2 subunit
  • part of the BCKAD complex
  • que
  • mitochondrial branched-chain alpha-keto acid dihydrolipoyl acyltransferase
  • component of branched chain keto acid dehydrogenase complex
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