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DLAT Produits

(Dihydrolipoyl Transacetylase (DLAT))

Catégories

This gene encodes component E2 of the multi-enzyme pyruvate dehydrogenase complex (PDC). PDC resides in the inner mitochondrial membrane and catalyzes the conversion of pyruvate to acetyl coenzyme A. The protein product of this gene, dihydrolipoamide acetyltransferase, accepts acetyl groups formed by the oxidative decarboxylation of pyruvate and transfers them to coenzyme A. Dihydrolipoamide acetyltransferase is the antigen for antimitochondrial antibodies. These autoantibodies are present in nearly 95% of patients with the autoimmune liver disease primary biliary cirrhosis (PBC). In PBC, activated T lymphocytes attack and destroy epithelial cells in the bile duct where this protein is abnormally distributed and overexpressed. PBC enventually leads to cirrhosis and liver failure. Mutations in this gene are also a cause of pyruvate dehydrogenase E2 deficiency which causes primary lactic acidosis in infancy and early childhood.[provided by RefSeq, Oct 2009].

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Catégories DLAT en vedette

DLAT Anticorps

High quality antibodies with extensive validation data.

DLAT Kits ELISA

Reliable ELISA kits for a wide range of species.

DLAT Protéines

Proteins for various applications incl. WB, ELISA, IF etc.

DLAT recommandé Anticorps

Produit
Reactivity
Application
Validations
N° du produit
Quantité
Fiche technique
Reactivity Mouse
Application WB, IHC, IP, ICC
Validations
  • (7)
N° du produit ABIN7432412
Quantité 100 μL
Fiche technique Fiche technique
Reactivity Human, Mouse, Rat
Application WB, IHC, IF
Validations
  • (5)
N° du produit ABIN7257932
Quantité 200 μL
Fiche technique Fiche technique
Reactivity Human
Application WB, IHC, IF
Validations
  • (5)
N° du produit ABIN7266768
Quantité 100 μL
Fiche technique Fiche technique

DLAT recommandé Kits ELISA

Produit
Reactivity
Analytical Method
Validations
N° du produit
Quantité
Fiche technique
Reactivity Mouse
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
N° du produit ABIN6966368
Quantité 96 tests
Fiche technique Fiche technique
Reactivity Mouse
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
N° du produit ABIN6955387
Quantité 96 tests
Fiche technique Fiche technique
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
N° du produit ABIN1114634
Quantité 96 tests
Fiche technique Fiche technique

DLAT recommandé Protéines

Produit
Reactivity
Source
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
N° du produit ABIN7122666
Quantité 50 μg
Fiche technique Fiche technique
Reactivity Human
Source Wheat germ
Validations
  • (1)
N° du produit ABIN1351656
Quantité 10 μg
Fiche technique Fiche technique
Reactivity Human
Source Insect Cells
Validations
  • (1)
N° du produit ABIN3085256
Quantité 1 mg
Fiche technique Fiche technique

Synonymes et noms alternatifs relatifs à DLAT

midline uncoordinated (muc), dihydrolipoamide S-acetyltransferase L homeolog (dlat.L), dihydrolipoamide S-acetyltransferase (DLAT), dihydrolipoamide S-acetyltransferase (Dlat), dihydrolipoamide S-acetyltransferase (E2 component of pyruvate dehydrogenase complex) (dlat), dihydrolipoamide S-acetyltransferase (E2 component of pyruvate dehydrogenase complex) (Dlat), 6332404G05Rik, anon-WO0118547.121, DLAT, DLTA, Dmel\\CG5261, EP(2)0816, EP816, PDC-E2, PDCE2, wu:fc14f10, wu:fc21f08, wu:fc86g11, wu:fj57d06

Protein level used designations for DLAT

  • CG5261-PA
  • CG5261-PB
  • CG5261-PC
  • CG5261-PD
  • CG5261-PE
  • CG5261-PF
  • Dihydrolipoyllysine-residue acetyltransferase
  • dihydrolipoamide acetyltransferase
  • dihydrolipoamide S-acetyltransferase (E2 component of pyruvate dehydrogenase complex)
  • 70 kDa mitochondrial autoantigen of primary biliary cirrhosis
  • E2 component of pyruvate dehydrogenase complex
  • M2 antigen complex 70 kDa subunit
  • PBC
  • dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex
  • dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex mitochondrial
  • dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, mitochondrial
  • pyruvate dehydrogenase complex component E2
  • dihydrolipoyllysine-residue acetyltransferase
  • E2
  • PDC-E2
  • PDCE2
  • fc86g11
  • fj57d06
  • no optokinetic nystagmus a
  • no optokinetic response b
  • noa
  • nrb
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