Tel:
+49 (0)241 95 163 153
Fax:
+49 (0)241 95 163 155
E-Mail:
orders@anticorps-enligne.fr

PEX19 Produits

(Peroxisomal Biogenesis Factor 19 (PEX19))

Catégories

This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is also known as PBD-CGJ. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Aug 2010].

antibodies-online.com est synonyme de produits de recherche de haute qualité. Cherchez, trouvez et commandez des outils avec des données de validation étendues, des images, des références. Notre service clientèle scientifique est toujours à votre disposition si vous avez des questions sur la sélection ou l'application de nos produits.

Catégories PEX19 en vedette

PEX19 Anticorps

High quality antibodies with extensive validation data.

PEX19 Protéines

Proteins for various applications incl. WB, ELISA, IF etc.

PEX19 recommandé Anticorps

Produit
Reactivity
Application
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Application WB, IF, ICC, IHC (p)
Validations
  • (5)
N° du produit ABIN2856772
Quantité 100 μL
Fiche technique Fiche technique
Reactivity Human
Application WB, ELISA
Validations
  • (3)
N° du produit ABIN519560
Quantité 100 μg
Fiche technique Fiche technique
Reactivity Human
Application WB, IHC, IF
Validations
  • (1)
  • (2)
N° du produit ABIN6145463
Quantité 100 μL
Fiche technique Fiche technique

PEX19 recommandé Kits ELISA

Produit
Reactivity
Analytical Method
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
N° du produit ABIN6231795
Quantité 96 tests
Fiche technique Fiche technique

PEX19 recommandé Protéines

Produit
Reactivity
Source
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
N° du produit ABIN7124370
Quantité 50 μg
Fiche technique Fiche technique
Reactivity Human
Source Wheat germ
Validations
  • (1)
N° du produit ABIN1314699
Quantité 10 μg
Fiche technique Fiche technique
Reactivity Human
Source Insect Cells
Validations
  • (1)
N° du produit ABIN3085862
Quantité 1 mg
Fiche technique Fiche technique

Dernières publications sur nos produits PEX19

Zhou, Yu, Arshad, Wang, Lu, Gong, Gu, Li, Xu: "Coordination Among Lipid Droplets, Peroxisomes, and Mitochondria Regulates Energy Expenditure Through the CIDE-ATGL-PPARα Pathway in Adipocytes." dans: Diabetes, Vol. 67, Issue 10, pp. 1935-1948, (2018) (PubMed).

Mayerhofer, Kattenfeld, Roscher, Muntau: "Two splice variants of human PEX19 exhibit distinct functions in peroxisomal assembly." dans: Biochemical and biophysical research communications, Vol. 291, Issue 5, pp. 1180-6, (2002) (PubMed).

Gloeckner, Mayerhofer, Landgraf, Muntau, Holzinger, Gerber, Kammerer, Adamski, Roscher: "Human adrenoleukodystrophy protein and related peroxisomal ABC transporters interact with the peroxisomal assembly protein PEX19p." dans: Biochemical and biophysical research communications, Vol. 271, Issue 1, pp. 144-50, (2000) (PubMed).

Synonymes et noms alternatifs relatifs à PEX19

Peroxin 19 (Pex19), Peroxisomal farnesylated protein (Bm1_19905), peroxisomal biogenesis factor 19 (PEX19), peroxisomal biogenesis factor 19 (Pex19), BEST:GH03076, CG5325, D1S2223E, DmelPex19, Dmel\\CG5325, HK33, PBD12A, Peroxin-19, PMP1, PMPI, PXF, Pxf, PxF, PXMP1

Protein level used designations for PEX19

  • CG5325-PA
  • CG5325-PB
  • Pex19-PA
  • Pex19-PB
  • peroxin 19
  • peroxisomal farnesylated protein
  • Peroxisomal farnesylated protein
  • 33 kDa housekeeping protein
  • housekeeping gene, 33kD
  • peroxin-19
  • peroxisome biogenesis factor 19
Vous êtes ici:
Support technique