FKRP anticorps (C-Term)

N° du produit ABIN1536611

Détail du produit anti-FKRP anticorps

Antigène: FKRP (Fukutin Related Protein (FKRP))

Épitope: AA 418-444, C-Term

Reactivité: Humain

Hôte: Souris

Clonalité: Monoclonal

Conjugué: Cet anticorp FKRP est non-conjugé

Application: Western Blotting (WB)

Homologie: M

Purification: This antibody is purified through a protein G column, followed by dialysis against PBS.

Immunogène: This FKRP antibody is generated from mice immunized with a KLH conjugated synthetic peptide between 418-444 amino acids from the C-terminal region of human FKRP.

Clone: 386CT13-1-9

Isotype: IgG1

Information d'application

Indications d'application: WB: 1:100

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: Purified monoclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: 4 °C,-20 °C

Stockage commentaire: FKRP Antibody (C-term) can be refrigerated at 2-8 °C for up to 6 months. For long term storage, keep at -20 °C.

Date de péremption: 6 months

Détails sur FKRP

Antigène: FKRP (Fukutin Related Protein (FKRP))

Autre désignation: FKRP (FKRP Produits)

Synonymes: anticorps zgc:162829, anticorps LGMD2I, anticorps MDC1C, anticorps MDDGA5, anticorps MDDGB5, anticorps MDDGC5, anticorps A830029B19Rik, anticorps AI842067, anticorps AI847300, anticorps LGMD1I, anticorps fukutin related protein, anticorps FKRP, anticorps fkrp, anticorps Fkrp

Sujet: This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq].

Poids moléculaire: 54568

ID gène: 79147

NCBI Accession: NP_001034974, NP_077277

UniProt: Q9H9S5

Pathways: Regulation of Carbohydrate Metabolic Process