FKRP anticorps (AA 30-220)

N° du produit ABIN6140666

Détail du produit anti-FKRP anticorps

Antigène: FKRP (Fukutin Related Protein (FKRP))

Épitope: AA 30-220

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp FKRP est non-conjugé

Application: Western Blotting (WB), Immunohistochemistry (IHC)

Séquence: QPRNSRARGP RRASAAGPRV TVLVREFEAF DNAVPELVDS FLQQDPAQPV VVAADTLPYP PLALPRIPNV RLALLQPALD RPAAASRPET YVATEFVALV PDGARAEAPG LLERMVEALR AGSARLVAAP VATANPARCL ALNVSLREWT ARYGAAPAAP RCDALDGDAV VLLRARDLFN LSAPLARPVG T

Réactivité croisée: Humain, Souris, Rat

Attributs du produit: Polyclonal Antibodies

Purification: Affinity purification

Immunogène: Recombinant fusion protein containing a sequence corresponding to amino acids 30-220 of human FKRP (NP_077277.1).

Isotype: IgG

Information d'application

Indications d'application: WB,1:1000 - 1:3000,IHC,1:50 - 1:200

Commentaires:

HIGH QUALITY

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur FKRP

Antigène: FKRP (Fukutin Related Protein (FKRP))

Autre désignation: FKRP (FKRP Produits)

Synonymes: anticorps zgc:162829, anticorps LGMD2I, anticorps MDC1C, anticorps MDDGA5, anticorps MDDGB5, anticorps MDDGC5, anticorps A830029B19Rik, anticorps AI842067, anticorps AI847300, anticorps LGMD1I, anticorps fukutin related protein, anticorps FKRP, anticorps fkrp, anticorps Fkrp

Sujet: This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined.,FKRP,LGMD2I,MDC1C,MDDGA5,MDDGB5,MDDGC5,Signal Transduction,FKRP

Poids moléculaire: 54 kDa

ID gène: 79147

UniProt: Q9H9S5

Pathways: Regulation of Carbohydrate Metabolic Process