GNS anticorps (C-Term)
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- Antigène Voir toutes GNS Anticorps
- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
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Épitope
- C-Term
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Reactivité
- Humain, Rat
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Hôte
- Lapin
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp GNS est non-conjugé
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Application
- Western Blotting (WB)
- Réactivité croisée
- Rat (Rattus)
- Purification
- Purified
- Immunogène
- Gns antibody was raised in rabbit using the C terminal of Gns as the immunogen
- Top Product
- Discover our top product GNS Anticorps primaire
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- Indications d'application
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WB: 0.2-1 µg/mL
Optimal conditions should be determined by the investigator. - Commentaires
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Gns Blocking Peptide, catalog no. 33R-10135, is also available for use as a blocking control in assays to test for specificity of this Gns antibody
- Restrictions
- For Research Use only
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- Format
- Lyophilized
- Concentration
- Lot specific
- Buffer
- Lyophilized powder. Add 50 µL of distilled water. Final antibody concentration is 1 mg/mL in PBS buffer.
- Conseil sur la manipulation
- Avoid repeated freeze/thaw cycles.
- Stock
- 4 °C/-20 °C
- Stockage commentaire
- Store at 4 °C, following reconstitution, aliquot and store at -20 °C.
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- Antigène
- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
- Autre désignation
- Gns (GNS Produits)
- Synonymes
- anticorps G6S, anticorps 2610016K11Rik, anticorps AU042285, anticorps C87209, anticorps N28088, anticorps NV14559, anticorps N-acetylglucosamine-6-sulfatase, anticorps zgc:114066, anticorps gns, anticorps wu:fi20h10, anticorps zgc:55370, anticorps glucosamine (N-acetyl)-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase S homeolog, anticorps glucosamine (N-acetyl)-6-sulfatase a, anticorps N-acetylglucosamine-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b, anticorps GNS, anticorps Gns, anticorps gns.S, anticorps gns, anticorps gnsa, anticorps CpipJ_CPIJ000745, anticorps Sros_7372, anticorps VDBG_04409, anticorps Halhy_3165, anticorps gnsb
- Sujet
- GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparin sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder ucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. Synonyms: Polyclonal Gns antibody, Anti-Gns antibody, glucosamine, N-acetyl-6-sulfatase antibody, Gns antibody.
- Pathways
- Glycosaminoglycan Metabolic Process
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