Aperçu des produits pour Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Kits ELISA

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Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Kits ELISA (HADHB)
Chez www.anticorps-enligne.fr sont 9 Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Kits ELISA de 5 de différents fournisseurs disponibles. De plus, nous expédions Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Anticorps (74) et Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Protéines (13) et beaucoup plus de produits pour cette protéine. Un total de 103 Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit produits sont actuellement listés.
Synonymes:
4930479F15Rik, ECHB, fb14g10, Hadhb, Mtpb, thiolase, TP-BETA, wu:fb14g10, zgc:56274

Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Kits ELISA par réactivité

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Human Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) interaction partners

  1. Exposure to bezafibrate (400 muM for 48 h) increased the abundance of HADHA (Montrer HADHA Kits ELISA) and HADHB mRNAs.

  2. nonstructural protein 5 (Montrer CAPS Kits ELISA) (NS5 (Montrer RAF1 Kits ELISA)) interacted with hydroxyacyl-CoA dehydrogenase (Montrer HADH Kits ELISA) alpha and beta subunits, two components of the mitochondrial trifunctional protein (MTP) involved in LCFA beta-oxidation

  3. Mutations in HADHB, which encodes the beta-subunit of mitochondrial trifunctional protein, cause infantile onset hypoparathyroidism and peripheral polyneuropathy.

  4. Heterozygous mutation in HADHB gene cause early-onset axonal axonal Charcot-Marie-tooth disease.

  5. The results demonstrated that ERbeta (Montrer ESR2 Kits ELISA) was indeed associated and colocalized with HADHB within mitochondria.

  6. HADHB is a functional molecular target of estrogen receptor alpha (Montrer ESR1 Kits ELISA) in the mitochondria, and the interaction may play an important role in the estrogen-mediated lipid metabolism in animals and humans.

  7. mutational analysis of the HADHB gene, which encodes long-chain 3-ketoacyl-CoA thiolase, identified compound heterozygous mutations of c.520C>T (p.R141C) and c.1331G>A (p.R411K) in a case of mitochondrial trifunctional protein deficiency

  8. Results emphasize the value of cDNA analysis in the characterization of HADHA (Montrer HADHA Kits ELISA) and HADHB mutations and further strengthen the model of haploinsufficiency as a major pathomechanism in MTP defects.

  9. Recombinant mitochondrial trifunctional protein displayed 2-enoyl-CoA hydratase, l-3-hydroxyacyl-CoA dehydrogenase, and 3-ketoacyl-CoA thiolase activities.

  10. The present findings showed that all missense mutations in HADHB were disease-causing.

Cow (Bovine) Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) interaction partners

  1. Mutation analysis of the HADHB gene of patient 4 identified compound heterozygosity of N114D/N307D.

Mouse (Murine) Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) interaction partners

  1. nonstructural protein 5 (Montrer CAPS Kits ELISA) (NS5 (Montrer RAF1 Kits ELISA)) interacted with hydroxyacyl-CoA dehydrogenase (Montrer HADH Kits ELISA) alpha and beta subunits, two components of the mitochondrial trifunctional protein (MTP (Montrer LAPTM4A Kits ELISA)) involved in LCFA beta-oxidation

Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) profil antigène

Antigen Summary

This gene encodes the beta subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the beta subunit catalyzing the 3-ketoacyl-CoA thiolase activity. Mutations in this gene result in trifunctional protein deficiency. The encoded protein can also bind RNA and decreases the stability of some mRNAs. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. Alternatively spliced transcript variants have been found\; however, their full-length nature is not known.

Alternative names and synonyms associated with Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB)

  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (HADHB) Elisa Kit
  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (hadhb) Elisa Kit
  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (Hadhb) Elisa Kit
  • hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit (hadhb) Elisa Kit
  • hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit (Hadhb) Elisa Kit
  • long-chain 3-ketoacyl-CoA thiolase (LCTHIO) Elisa Kit
  • 4930479F15Rik Elisa Kit
  • ECHB Elisa Kit
  • fb14g10 Elisa Kit
  • Hadhb Elisa Kit
  • Mtpb Elisa Kit
  • thiolase Elisa Kit
  • TP-BETA Elisa Kit
  • wu:fb14g10 Elisa Kit
  • zgc:56274 Elisa Kit

Protein level used designations for HADHB

2-enoyl-Coenzyme A (CoA) hydratase, beta subunit , 3-ketoacyl-Coenzyme A (CoA) thiolase of mitochondrial trifunctional protein, beta subunit , acetyl-CoA acyltransferase , beta-ketothiolase , hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit , trifunctional enzyme subunit beta, mitochondrial , hydroxyacyl dehydrogenase, subunit B , TP-beta , dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit , mitochondrial trifunctional protein, beta subunit , 3-ketoacyl-Coenzyme A thiolase , TP-Beta , enoyl-Coenzyme A hydratase, beta subunit , trifunctional enzyme beta subunit, mitochondrial , dehydrogenase/3-ketoacyl-Coenzyme A thiolase , hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta aubunit

GENE ID SPECIES
3032 Homo sapiens
379769 Xenopus laevis
421995 Gallus gallus
281811 Bos taurus
171155 Rattus norvegicus
607926 Canis lupus familiaris
459080 Pan troglodytes
336606 Danio rerio
231086 Mus musculus
397017 Sus scrofa
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