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ALDH6A1 Produits

(Aldehyde Dehydrogenase 6 Family, Member A1 (ALDH6A1))

Catégories

This protein belongs to the aldehyde dehydrogenases family of proteins. This enzyme plays a role in the valine and pyrimidine catabolic pathways. The product of this gene, a mitochondrial methylmalonate semialdehyde dehydrogenase, catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids. [provided by RefSeq, Jul 2008].

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Catégories ALDH6A1 en vedette

ALDH6A1 Anticorps

High quality antibodies with extensive validation data.

ALDH6A1 Kits ELISA

Reliable ELISA kits for a wide range of species.

ALDH6A1 Protéines

Proteins for various applications incl. WB, ELISA, IF etc.

ALDH6A1 recommandé Anticorps

Produit
Reactivity
Application
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Application WB, ELISA, IHC, FACS, ICC
Validations
  • (9)
N° du produit ABIN5542265
Quantité 0.1 mg
Fiche technique Fiche technique
Reactivity Human
Application WB, IHC (p), IF
Validations
  • (4)
N° du produit ABIN659006
Quantité 400 μL
Fiche technique Fiche technique
Reactivity Human
Application WB, IHC (p)
Validations
  • (4)
N° du produit ABIN2855626
Quantité 100 μL
Fiche technique Fiche technique

ALDH6A1 recommandé Kits ELISA

Produit
Reactivity
Analytical Method
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
N° du produit ABIN6953596
Quantité 96 tests
Fiche technique Fiche technique
Reactivity Mouse
Analytical Method
Validations
N° du produit ABIN1142386
Quantité 96 tests
Fiche technique Fiche technique
Reactivity Rat
Analytical Method
Validations
N° du produit ABIN1142387
Quantité 96 tests
Fiche technique Fiche technique

ALDH6A1 recommandé Protéines

Produit
Reactivity
Source
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Source Wheat germ
Validations
  • (1)
N° du produit ABIN1344841
Quantité 10 μg
Fiche technique Fiche technique
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
N° du produit ABIN7121777
Quantité 50 μg
Fiche technique Fiche technique
Reactivity Human
Source Insect Cells
Validations
  • (1)
N° du produit ABIN3083766
Quantité 1 mg
Fiche technique Fiche technique

Dernières publications sur nos produits ALDH6A1

Jeon, Jeong, Baek, Koo, Park, Yang, Yu, Kim, Pak: "Network clustering revealed the systemic alterations of mitochondrial protein expression." dans: PLoS computational biology, Vol. 7, Issue 6, pp. e1002093, (2011) (PubMed).

Alnouti, Klaassen: "Tissue distribution, ontogeny, and regulation of aldehyde dehydrogenase (Aldh) enzymes mRNA by prototypical microsomal enzyme inducers in mice." dans: Toxicological sciences : an official journal of the Society of Toxicology, Vol. 101, Issue 1, pp. 51-64, (2007) (PubMed).

Kuiper, Williams, Distl, Drögemüller: "Assignment of the PAX6 gene to bovine chromosome 15q25-->q27 by fluorescence in situ hybridization and confirmation by radiation hybrid mapping." dans: Cytogenetic and genome research, Vol. 109, Issue 4, pp. 533, (2005) (PubMed).

Anderson, Polanski, Pieper, Gatlin, Tirumalai, Conrads, Veenstra, Adkins, Pounds, Fagan, Lobley: "The human plasma proteome: a nonredundant list developed by combination of four separate sources." dans: Molecular & cellular proteomics : MCP, Vol. 3, Issue 4, pp. 311-26, (2004) (PubMed).

Chambliss, Gray, Rylance, Pollitt, Gibson: "Molecular characterization of methylmalonate semialdehyde dehydrogenase deficiency." dans: Journal of inherited metabolic disease, Vol. 23, Issue 5, pp. 497-504, (2000) (PubMed).

Synonymes et noms alternatifs relatifs à ALDH6A1

aldehyde dehydrogenase 6 family member A1 (ALDH6A1), aldehyde dehydrogenase 6 family, member A1 (Aldh6a1), aldehyde dehydrogenase 6 family member A1 L homeolog (aldh6a1.L), methylmalonic acid semialdehyde dehydrogenase (CCNA_02357), aldehyde dehydrogenase 6 family, member A1 (aldh6a1), methylmalonate-semialdehyde dehydrogenase (CoA acylating) (VAA_RS07845), aldehyde dehydrogenase family 6, subfamily A1 (Aldh6a1), aldehyde dehydrogenase 6 family member A1 (Aldh6a1), 1110038I05Rik, AI314632, cb850, MMSADHA, MMSDH, Mmsdh, wu:fb03a04, zgc:92082

Protein level used designations for ALDH6A1

  • malonate-semialdehyde dehydrogenase
  • methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
  • mitochondrial acylating methylmalonate-semialdehyde dehydrogenase
  • aldehyde dehydrogenase family 6 member A1
  • aldehyde dehydrogenase family 6, subfamily A1
  • methylmalonate semialdehyde dehydrogenase
  • MMSDH
  • aldehyde dehydrogenase 6A1
  • aldehyde dehydrogenase 6 family, member A1
  • methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial-like
  • Malonate-semialdehyde dehydrogenase
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