Optimal working dilution should be determined by the investigator.
Restrictions
For Research Use only
Reconstitution
Add 50 μL of distilled water to a final concentration of 1 mg/mL.
Conseil sur la manipulation
Avoid repeated freezing and thawing.
Stock
4 °C/-20 °C
Stockage commentaire
Store lyophilized at 2-8 °C or at -20 °C long term. After reconstitution store the antibody undiluted at 2-8 °C for up to one month or in aliquots at -20 °C long term.
Antigène
ACADL
(Acyl-CoA Dehydrogenase, Long Chain (ACADL))
anticorps zgc:55656, anticorps ACAD4, anticorps LCAD, anticorps ACOADA, anticorps AA960361, anticorps AU018452, anticorps C79855, anticorps acyl-CoA dehydrogenase long chain, anticorps acyl-CoA dehydrogenase, long chain, anticorps acyl-CoA dehydrogenase, long chain L homeolog, anticorps acyl-Coenzyme A dehydrogenase, long-chain, anticorps acadl, anticorps ACADL, anticorps Acadl, anticorps acadl.L
Sujet
ACADL belongs to the acyl-CoA dehydrogenase family, which is a family of mitochondrial flavoenzymes involved in fatty acid and branched chain amino-acid metabolism. This protein is one of the four enzymes that catalyze the initial step of mitochondrial beta-oxidation of straight-chain fatty acid. Defects in ACADL gene are the cause of long-chain acyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia.The protein encoded by this gene belongs to the acyl-CoA dehydrogenase family, which is a family of mitochondrial flavoenzymes involved in fatty acid and branched chain amino-acid metabolism. This protein is one of the four enzymes that catalyze the initial step of mitochondrial beta-oxidation of straight-chain fatty acid. Defects in this gene are the cause of long-chain acyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia.Synonyms: LCAD, Long-chain specific acyl-CoA dehydrogenase, mitochondrial