ALAS2 anticorps

N° du produit ABIN2462494

Détail du produit anti-ALAS2 anticorps

Antigène: ALAS2 (Aminolevulinate, delta-, Synthase 2 (ALAS2))

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp ALAS2 est non-conjugé

Application: Western Blotting (WB), ELISA, Immunohistochemistry (IHC)

Purification: Antibody is purified by protein A chromatography method.

Immunogène: Antibody produced in rabbits immunized with a synthetic peptide corresponding a region of human ALAS2.

Information d'application

Indications d'application: ALAS2 antibody can be used for detection of ALAS2 by ELISA at 1:62500. ALAS2 antibody can be used for detection of ALAS2 by western blot at 5.0 μg/mL, and HRP conjugated secondary antibody should be diluted 1:50,000 - 100,000.

Restrictions: For Research Use only

Stockage

Format: Lyophilized

Reconstitution: Add 100 ?L of distilled water. Final antibody concentration is 1 mg/mL.

Concentration: 1 mg/mL

Buffer: Antibody is lyophilized in PBS buffer with 2 % sucrose.

Conseil sur la manipulation: As with any antibody avoid repeat freeze-thaw cycles.

Stock: 4 °C/-20 °C

Stockage commentaire: For short periods of storage (days) store at 4 °C. For longer periods of storage, store ALAS2 antibody at -20 °C.

Détails sur ALAS2

Antigène: ALAS2 (Aminolevulinate, delta-, Synthase 2 (ALAS2))

Autre désignation: ALAS2 (ALAS2 Produits)

Synonymes: anticorps anh1, anticorps asb, anticorps xlsa, anticorps ALAS-E, anticorps ALASE, anticorps ANH1, anticorps ASB, anticorps XLDPP, anticorps XLEPP, anticorps XLSA, anticorps alas-e, anticorps cb1063, anticorps sau, anticorps sauternes, anticorps ALAS, anticorps Alas-2, anticorps 5'-aminolevulinate synthase 2, anticorps aminolevulinate, delta-, synthase 2, anticorps aminolevulinic acid synthase 2, erythroid, anticorps alas2, anticorps ALAS2, anticorps Alas2, anticorps alas2.L

Sujet: ALAS2 specifies an erythroid-specific mitochondrially located enzyme. The protein catalyzes the first step in the heme biosynthetic pathway. Defects in its gene cause X-linked pyridoxine-responsive sideroblastic anemia.The product of this gene specifies an erythroid-specific mitochondrially located enzyme. The encoded protein catalyzes the first step in the heme biosynthetic pathway. Defects in this gene cause X-linked pyridoxine-responsive sideroblastic anemia. Alternatively spliced transcript variants encoding different isoforms have been identified.

Poids moléculaire: 57 kDa, 65 kDa, 61 kDa, 63 kDa

ID gène: 212

NCBI Accession: NP_001033058

UniProt: P22557

Pathways: Transition Metal Ion Homeostasis