PEX12 anticorps (Middle Region)

N° du produit ABIN5515310

Détail du produit anti-PEX12 anticorps

Antigène: PEX12 (Peroxisomal Biogenesis Factor 12 (PEX12))

Épitope: Middle Region

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp PEX12 est non-conjugé

Application: Western Blotting (WB)

Séquence: SIMFLVLLPY LKVKLEKLVS SLREEDEYSI HPPSSRWKRF YRAFLAAYPF

Purification: Affinity purified

Immunogène: The immunogen is a synthetic peptide directed towards the middle region of human PEX12

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Détails sur PEX12

Antigène: PEX12 (Peroxisomal Biogenesis Factor 12 (PEX12))

Autre désignation: PEX12 (PEX12 Produits)

Synonymes: anticorps zgc:56182, anticorps pex12, anticorps MGC81372, anticorps PEX12, anticorps DDBDRAFT_0186545, anticorps DDBDRAFT_0238076, anticorps DDB_0186545, anticorps DDB_0238076, anticorps LOC100226224, anticorps PAF-3, anticorps PBD3A, anticorps Peroxin-12, anticorps AI451906, anticorps peroxisomal biogenesis factor 12, anticorps peroxisomal biogenesis factor 12 L homeolog, anticorps RING zinc finger-containing protein, anticorps pex12, anticorps PEX12, anticorps pex12.L, anticorps Pex12

Sujet: This gene belongs to the peroxin-12 family. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS).

Alias Symbols: PAF-3, PBD3A

Protein Size: 167

ID gène: 5193

NCBI Accession: NM_000286, NP_000277

UniProt: O00623