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L2HGDH anticorps (AA 1-220)

L2HGDH Reactivité: Humain WB Hôte: Lapin Polyclonal unconjugated
N° du produit ABIN6143055
  • Antigène Voir toutes L2HGDH Anticorps
    L2HGDH (L-2-Hydroxyglutarate Dehydrogenase (L2HGDH))
    Épitope
    • 7
    • 7
    • 7
    • 6
    • 5
    • 5
    • 4
    • 2
    • 1
    • 1
    AA 1-220
    Reactivité
    • 31
    • 15
    • 6
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    Humain
    Hôte
    • 36
    Lapin
    Clonalité
    • 36
    Polyclonal
    Conjugué
    • 18
    • 6
    • 4
    • 4
    • 2
    • 2
    Cet anticorp L2HGDH est non-conjugé
    Application
    • 26
    • 25
    • 9
    • 2
    • 1
    Western Blotting (WB)
    Séquence
    MVPALRYLVG ACGRARGLFA GGSPGACGFA SGRPRPLCGG SRSASTSSFD IVIVGGGIVG LASARALILR HPSLSIGVLE KEKDLAVHQT GHNSGVIHSG IYYKPESLKA KLCVQGAALL YEYCQQKGIS YKQCGKLIVA VEQEEIPRLQ ALYEKGLQNG VPGLRLIQQE DIKKKEPYCR GLMAIDCPHT GIVDYRQVAL SFAQDFQEAG GSVLTNFEVK
     Réactivité croisée
    Humain, Souris
    Attributs du produit
    Polyclonal Antibodies
    Immunogène
    Recombinant fusion protein containing a sequence corresponding to amino acids 1-220 of human L2HGDH (NP_079160.1).
    Isotype
    IgG
    Top Product
    Discover our top product L2HGDH Anticorps primaire
  • Indications d'application
    WB,1:500 - 1:2000
    Commentaires

    HIGH QUALITY

    Restrictions
    For Research Use only
  • Format
    Liquid
    Buffer
    PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
    Agent conservateur
    Sodium azide
    Précaution d'utilisation
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Stock
    -20 °C
    Stockage commentaire
    Store at -20°C. Avoid freeze / thaw cycles.
  • Antigène
    L2HGDH (L-2-Hydroxyglutarate Dehydrogenase (L2HGDH))
    Autre désignation
    L2HGDH (L2HGDH Produits)
    Synonymes
    anticorps RGD1306250, anticorps C14orf160, anticorps BC016226, anticorps L-2-hydroxyglutarate dehydrogenase, anticorps L2hgdh, anticorps L2HGDH
    Sujet
    This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation.,L2HGDH,C14orf160,L2HGA,Signal Transduction,Cell Biology & Developmental Biology,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,L2HGDH
    Poids moléculaire
    48 kDa/50 kDa
    ID gène
    79944
    UniProt
    Q9H9P8
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