BCKDHB anticorps (N-Term)

N° du produit ABIN654629

Détail du produit anti-BCKDHB anticorps

Antigène: BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))

Épitope: AA 41-70, N-Term

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp BCKDHB est non-conjugé

Application: Western Blotting (WB), Flow Cytometry (FACS), Immunofluorescence (IF), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))

Purification: This antibody is purified through a protein A column, followed by peptide affinity purification.

Immunogène: This BCKDHB antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 41-70 amino acids from the N-terminal region of human BCKDHB.

Clone: RB20925

Isotype: Ig Fraction

Information d'application

Indications d'application: IF: 1:25. WB: 1:1000. WB: 1:1000. IHC-P-Leica: 1:500. IHC-P-Leica: 1:500. FC: 1:10~50

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: Purified polyclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: 4 °C,-20 °C

Stockage commentaire: Maintain refrigerated at 2-8 °C for up to 6 months. For long term storage store at -20 °C in small aliquots to prevent freeze-thaw cycles.

Date de péremption: 6 months

Détails sur BCKDHB

Antigène: BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))

Autre désignation: BCKDHB (BCKDHB Produits)

Synonymes: anticorps zgc:158777, anticorps BCKDHB, anticorps E1B, anticorps dJ279A18.1, anticorps branched chain keto acid dehydrogenase E1, beta polypeptide, anticorps branched chain keto acid dehydrogenase E1 subunit beta, anticorps branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog, anticorps branched chain ketoacid dehydrogenase E1, beta polypeptide, anticorps BCKDHB, anticorps bckdhb, anticorps bckdhb.S, anticorps Bckdhb

Sujet: Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems.

Poids moléculaire: 43122

ID gène: 594

NCBI Accession: NP_000047, NP_898871

UniProt: P21953