BCKDHB anticorps (N-Term)

N° du produit ABIN950620

Détail du produit anti-BCKDHB anticorps

Antigène: BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))

Épitope: AA 44-74, N-Term

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp BCKDHB est non-conjugé

Application: Western Blotting (WB), Flow Cytometry (FACS), Immunofluorescence (IF), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Enzyme Immunoassay (EIA)

Specificité: This antibody reacts to BCKDHB.

Réactivité croisée (Details): Species reactivity (tested):Human.

Purification: Affinity chromatography on Protein A

Immunogène: KLH conjugated synthetic peptide between 44-74 amino acids from the N-terminal region of human BCKDHB

Isotype: Ig Fraction

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.25 mg/mL

Buffer: PBS containing 0.09 % (W/V) sodium azide as preservative

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeated freezing and thawing.

Stock: 4 °C/-20 °C

Stockage commentaire: Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.

Détails sur BCKDHB

Antigène: BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))

Autre désignation: BCKDHB (BCKDHB Produits)

Synonymes: anticorps zgc:158777, anticorps BCKDHB, anticorps E1B, anticorps dJ279A18.1, anticorps branched chain keto acid dehydrogenase E1, beta polypeptide, anticorps branched chain keto acid dehydrogenase E1 subunit beta, anticorps branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog, anticorps branched chain ketoacid dehydrogenase E1, beta polypeptide, anticorps BCKDHB, anticorps bckdhb, anticorps bckdhb.S, anticorps Bckdhb

Sujet: Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems.Synonyms: 2-oxoisovalerate dehydrogenase subunit beta, alpha-keto acid dehydrogenase, mitochondrial Branched-chain alpha-keto acid dehydrogenase E1 component beta chain

ID gène: 594

NCBI Accession: NP_000047