FH anticorps (AA 411-510) (Alexa Fluor 488)

N° du produit ABIN897948

Détail du produit anti-FH anticorps (Alexa Fluor 488)

Antigène: FH (Fumarate Hydratase (FH))

Épitope: AA 411-510

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp FH est conjugé à/à la Alexa Fluor 488

Application: Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))

Homologie: Human,Mouse,Rat,Dog,Cow,Sheep,Pig,Horse,Rabbit

Purification: Purified by Protein A.

Immunogène: KLH conjugated synthetic peptide derived from human Fumarate hydratase (447-496aa)

Isotype: IgG

Information d'application

Indications d'application: IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 μg/μL

Buffer: Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.

Agent conservateur: ProClin

Précaution d'utilisation: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

Date de péremption: 12 months

Détails sur FH

Antigène: FH (Fumarate Hydratase (FH))

Autre désignation: Fumarate hydratase/FH (FH Produits)

Synonymes: anticorps FH, anticorps DDBDRAFT_0205237, anticorps DDBDRAFT_0231397, anticorps DDBDRAFT_0231400, anticorps DDB_0205237, anticorps DDB_0231397, anticorps DDB_0231400, anticorps HLRCC, anticorps LRCC, anticorps MCL, anticorps MCUL1, anticorps Fh1, anticorps im:7152785, anticorps ns:zf-e152, anticorps zf-e152, anticorps zgc:66253, anticorps zgc:77498, anticorps Fh, anticorps Fh-1, anticorps fumarate hydratase, anticorps fumarate hydratase 1, anticorps FH, anticorps fumH, anticorps Fh, anticorps fh, anticorps Fh1

Sujet:

Synonyms: mitochondrial, FH, Fumarase, Fumarate hydratase, Fumarate hydratase mitochondrial, FUMH_HUMAN, HLRCC, LRCC, MCL, MCUL 1, MCUL1, Multiple hereditary cutaneous leiomyomata.

Background: Defects in FH are the cause of fumarase deficiency (FHD)also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.

ID gène: 2271