GNS anticorps (AA 174-203)
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- Antigène Voir toutes GNS Anticorps
- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
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Épitope
- AA 174-203
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Reactivité
- Humain
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Hôte
- Lapin
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp GNS est non-conjugé
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Application
- Western Blotting (WB), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
- Purification
- This antibody is prepared by Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis
- Immunogène
- This GNS antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 174-203 amino acids from the Central region of human GNS.
- Isotype
- Ig Fraction
- Top Product
- Discover our top product GNS Anticorps primaire
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- Indications d'application
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For WB starting dilution is: 1:1000
For IHC-P starting dilution is: 1:50~100 - Restrictions
- For Research Use only
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- Format
- Liquid
- Concentration
- 2 mg/mL
- Buffer
- Supplied in PBS with 0.09 % (W/V) sodium azide.
- Agent conservateur
- Sodium azide
- Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Stock
- 4 °C,-20 °C
- Stockage commentaire
- Store at 4°C for three months and -20°C, stable for up to one year. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.
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- Antigène
- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
- Autre désignation
- GNS (GNS Produits)
- Synonymes
- anticorps G6S, anticorps 2610016K11Rik, anticorps AU042285, anticorps C87209, anticorps N28088, anticorps NV14559, anticorps N-acetylglucosamine-6-sulfatase, anticorps zgc:114066, anticorps gns, anticorps wu:fi20h10, anticorps zgc:55370, anticorps glucosamine (N-acetyl)-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase S homeolog, anticorps glucosamine (N-acetyl)-6-sulfatase a, anticorps N-acetylglucosamine-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b, anticorps GNS, anticorps Gns, anticorps gns.S, anticorps gns, anticorps gnsa, anticorps CpipJ_CPIJ000745, anticorps Sros_7372, anticorps VDBG_04409, anticorps Halhy_3165, anticorps gnsb
- Sujet
- GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
- Poids moléculaire
- 62 kDa
- ID gène
- 2799
- UniProt
- P15586
- Pathways
- Glycosaminoglycan Metabolic Process
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