BCKDHB anticorps (AA 183-392)

N° du produit ABIN6137489

Détail du produit anti-BCKDHB anticorps

Antigène: BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))

Épitope: AA 183-392

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp BCKDHB est non-conjugé

Application: Western Blotting (WB)

Séquence: RSPWGCVGHG ALYHSQSPEA FFAHCPGIKV VIPRSPFQAK GLLLSCIEDK NPCIFFEPKI LYRAAAEEVP IEPYNIPLSQ AEVIQEGSDV TLVAWGTQVH VIREVASMAK EKLGVSCEVI DLRTIIPWDV DTICKSVIKT GRLLISHEAP LTGGFASEIS STVQEECFLN LEAPISRVCG YDTPFPHIFE PFYIPDKWKC YDALRKMINY

Réactivité croisée: Souris

Attributs du produit: Polyclonal Antibodies

Purification: Affinity purification

Immunogène: Recombinant fusion protein containing a sequence corresponding to amino acids 183-392 of human BCKDHB (NP_898871.1).

Isotype: IgG

Information d'application

Indications d'application: WB,1:500 - 1:2000

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur BCKDHB

Antigène: BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))

Autre désignation: BCKDHB (BCKDHB Produits)

Synonymes: anticorps zgc:158777, anticorps BCKDHB, anticorps E1B, anticorps dJ279A18.1, anticorps branched chain keto acid dehydrogenase E1, beta polypeptide, anticorps branched chain keto acid dehydrogenase E1 subunit beta, anticorps branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog, anticorps branched chain ketoacid dehydrogenase E1, beta polypeptide, anticorps BCKDHB, anticorps bckdhb, anticorps bckdhb.S, anticorps Bckdhb

Sujet: This gene encodes the E1 beta subunit of branched-chain keto acid dehydrogenase, which is a multienzyme complex associated with the inner membrane of mitochondria. This enzyme complex functions in the catabolism of branched-chain amino acids. Mutations in this gene have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation and feeding problems. Alternative splicing at this locus results in multiple transcript variants.,BCKDHB,BCKDE1B,BCKDH E1-beta,E1B,BCKDHE1-beta,Cancer,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Amino acid metabolism,BCKDHB

Poids moléculaire: 23 kDa/43 kDa

ID gène: 594

UniProt: P21953