GNS anticorps (AA 293-552)

N° du produit ABIN6141262

Détail du produit anti-GNS anticorps

Antigène: GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

Épitope: AA 293-552

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp GNS est non-conjugé

Application: Western Blotting (WB)

Séquence: WQTLLSVDDL VEKLVKRLEF TGELNNTYIF YTSDNGYHTG QFSLPIDKRQ LYEFDIKVPL LVRGPGIKPN QTSKMLVANI DLGPTILDIA GYDLNKTQMD GMSLLPILRG ASNLTWRSDV LVEYQGEGRN VTDPTCPSLS PGVSQCFPDC VCEDAYNNTY ACVRTMSALW NLQYCEFDDQ EVFVEVYNLT ADPDQITNIA KTIDPELLGK MNYRLMMLQS CSGPTCRTPG VFDPGYRFDP RLMFSNRGSV RTRRFSKHLL

Réactivité croisée: Humain, Souris, Rat

Attributs du produit: Polyclonal Antibodies

Purification: Affinity purification

Immunogène: Recombinant fusion protein containing a sequence corresponding to amino acids 293-552 of human GNS (NP_002067.1).

Isotype: IgG

Information d'application

Indications d'application: WB,1:500 - 1:2000

Commentaires:

HIGH QUALITY

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur GNS

Antigène: GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

Autre désignation: GNS (GNS Produits)

Synonymes: anticorps G6S, anticorps 2610016K11Rik, anticorps AU042285, anticorps C87209, anticorps N28088, anticorps NV14559, anticorps N-acetylglucosamine-6-sulfatase, anticorps zgc:114066, anticorps gns, anticorps wu:fi20h10, anticorps zgc:55370, anticorps glucosamine (N-acetyl)-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase S homeolog, anticorps glucosamine (N-acetyl)-6-sulfatase a, anticorps N-acetylglucosamine-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b, anticorps GNS, anticorps Gns, anticorps gns.S, anticorps gns, anticorps gnsa, anticorps CpipJ_CPIJ000745, anticorps Sros_7372, anticorps VDBG_04409, anticorps Halhy_3165, anticorps gnsb

Sujet: The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.,GNS,G6S,Cancer,Signal Transduction,Cell Biology & Developmental Biology,Ubiquitin,Endocrine & Metabolism,Amino acid metabolism,GNS

Poids moléculaire: 59 kDa/62 kDa

ID gène: 2799

UniProt: P15586

Pathways: Glycosaminoglycan Metabolic Process