GNS anticorps (AA 293-552)
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- Antigène Voir toutes GNS Anticorps
- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
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Épitope
- AA 293-552
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Reactivité
- Humain
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Hôte
- Lapin
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp GNS est non-conjugé
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Application
- Western Blotting (WB)
- Séquence
- WQTLLSVDDL VEKLVKRLEF TGELNNTYIF YTSDNGYHTG QFSLPIDKRQ LYEFDIKVPL LVRGPGIKPN QTSKMLVANI DLGPTILDIA GYDLNKTQMD GMSLLPILRG ASNLTWRSDV LVEYQGEGRN VTDPTCPSLS PGVSQCFPDC VCEDAYNNTY ACVRTMSALW NLQYCEFDDQ EVFVEVYNLT ADPDQITNIA KTIDPELLGK MNYRLMMLQS CSGPTCRTPG VFDPGYRFDP RLMFSNRGSV RTRRFSKHLL
- Réactivité croisée
- Humain, Souris, Rat
- Attributs du produit
- Polyclonal Antibodies
- Purification
- Affinity purification
- Immunogène
- Recombinant fusion protein containing a sequence corresponding to amino acids 293-552 of human GNS (NP_002067.1).
- Isotype
- IgG
- Top Product
- Discover our top product GNS Anticorps primaire
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- Indications d'application
- WB,1:500 - 1:2000
- Commentaires
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HIGH QUALITY
- Restrictions
- For Research Use only
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- Format
- Liquid
- Buffer
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
- Agent conservateur
- Sodium azide
- Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Stock
- -20 °C
- Stockage commentaire
- Store at -20°C. Avoid freeze / thaw cycles.
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- Antigène
- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
- Autre désignation
- GNS (GNS Produits)
- Synonymes
- anticorps G6S, anticorps 2610016K11Rik, anticorps AU042285, anticorps C87209, anticorps N28088, anticorps NV14559, anticorps N-acetylglucosamine-6-sulfatase, anticorps zgc:114066, anticorps gns, anticorps wu:fi20h10, anticorps zgc:55370, anticorps glucosamine (N-acetyl)-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase S homeolog, anticorps glucosamine (N-acetyl)-6-sulfatase a, anticorps N-acetylglucosamine-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b, anticorps GNS, anticorps Gns, anticorps gns.S, anticorps gns, anticorps gnsa, anticorps CpipJ_CPIJ000745, anticorps Sros_7372, anticorps VDBG_04409, anticorps Halhy_3165, anticorps gnsb
- Sujet
- The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.,GNS,G6S,Cancer,Signal Transduction,Cell Biology & Developmental Biology,Ubiquitin,Endocrine & Metabolism,Amino acid metabolism,GNS
- Poids moléculaire
- 59 kDa/62 kDa
- ID gène
- 2799
- UniProt
- P15586
- Pathways
- Glycosaminoglycan Metabolic Process
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