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Hexosaminidase A anticorps
HEXA
Reactivité: Humain, Souris, Rat
WB, IHC
Hôte: Lapin
Polyclonal
unconjugated
N° du produit ABIN6290114
Détail du produit anti-Hexosaminidase A anticorps
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Antigène
Voir toutes Hexosaminidase A (HEXA) Anticorps
Hexosaminidase A (HEXA)
Reactivité
Toutes les réactivités sur Hexosaminidase A Anticorps
Humain, Souris, Rat
Hôte
Toutes les hôtes sur Hexosaminidase A Anticorps
Lapin
Clonalité
Toutes les clonalités sur Hexosaminidase A Anticorps
Polyclonal
Conjugué
Tous les conjugués à travers Hexosaminidase A Anticorps
Cet anticorp Hexosaminidase A est non-conjugé
Application
Tous les applications à travers Hexosaminidase A Anticorps.
Western Blotting (WB), Immunohistochemistry (IHC)
Purification
Affinity purification
Immunogène
Recombinant protein of human HEXA
Isotype
IgG
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Discover our top product HEXA Anticorps primaire
Alternatives
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Information d'application
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Indications d'application
WB 1:500 - 1:2000 IHC 1:50 - 1:200
Restrictions
For Research Use only
Stockage
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Buffer
PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3.
Agent conservateur
Sodium azide
Précaution d'utilisation
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Stock
-20 °C
Stockage commentaire
Store at -20C. Avoid freeze / thaw cycles.
Détails sur Hexosaminidase A
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Antigène
Hexosaminidase A (HEXA)
Autre désignation
HEXA (HEXA Produits )
Synonymes
anticorps TSD, anticorps fc04h11, anticorps wu:fc04h11, anticorps wu:fv09f06, anticorps si:dkey-35i22.2, anticorps HEXA, anticorps Hex-1, anticorps zgc:112084, anticorps hexosaminidase subunit alpha, anticorps hexosaminidase B (beta polypeptide), anticorps CUGBP Elav-like family member 6, anticorps hexosaminidase A, anticorps hexosaminidase A (alpha polypeptide), anticorps beta-hexosaminidase subunit alpha-like, anticorps HEXA, anticorps hexb, anticorps CELF6, anticorps Hexa, anticorps hexa, anticorps LOC100228061
Sujet
This gene encodes a member of the glycosyl hydrolase 20 family of proteins. The encoded preproprotein is proteolytically processed to generate the alpha subunit of the lysosomal enzyme beta-hexosaminidase. This enzyme, together with the cofactor GM2 activator protein, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Mutations in this gene lead to an accumulation of GM2 ganglioside in neurons, the underlying cause of neurodegenerative disorders termed the GM2 gangliosidoses, including Tay-Sachs disease (GM2-gangliosidosis type I). Alternative splicing results in multiple transcript variants, at least one of which encodes a preproprotein that is proteolytically processed.
Poids moléculaire
60.703 kDa
ID gène
3073
UniProt
P06865
Pathways
Sensory Perception of Sound , Glycosaminoglycan Metabolic Process
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