GBA anticorps

N° du produit ABIN7267407

Détail du produit anti-GBA anticorps

Antigène: GBA (Glucosidase, Beta, Acid (GBA))

Reactivité: Humain

Hôte: Lapin

Clonalité: Monoclonal

Conjugué: Cet anticorp GBA est non-conjugé

Application: Western Blotting (WB), Immunohistochemistry (IHC)

Fonction: Glucosylceramidase beta (GBA) Rabbit mAb

Réactivité croisée: Humain, Rat

Attributs du produit: Monoclonal Antibodies

Purification: Affinity purification

Immunogène: A synthesized peptide derived from human Glucosylceramidase beta (Glucosylceramidase beta (GBA))

Isotype: IgG

Information d'application

Indications d'application: WB,1:500 - 1:2000,IHC,1:50 - 1:200

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,0.05 % BSA,50 % glycerol, pH 7.3.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur GBA

Antigène: GBA (Glucosidase, Beta, Acid (GBA))

Autre désignation: GBA (GBA Produits)

Synonymes: anticorps GBA1, anticorps GCB, anticorps GLUC, anticorps BETA-GLUCOSIDASE, anticorps T12J13.8, anticorps T12J13_8, anticorps beta glucosidase 25, anticorps PSPTO3318, anticorps PSPTO4290, anticorps GC, anticorps GCase, anticorps betaGC, anticorps glucosylceramidase beta, anticorps beta glucosidase 25, anticorps beta-glucosidase, anticorps Beta-glucosidase, anticorps glucosidase, beta, acid, anticorps glucosylceramidase, anticorps bglX-2, anticorps GBA, anticorps BGLU25, anticorps PSPTO_3318, anticorps bglX, anticorps bglA4, anticorps Gba, anticorps LOC100399524, anticorps bglA.2, anticorps bglX-2

Sujet: This gene encodes a lysosomal membrane protein that cleaves the beta-glucosidic linkage of glycosylceramide, an intermediate in glycolipid metabolism. Mutations in this gene cause Gaucher disease, a lysosomal storage disease characterized by an accumulation of glucocerebrosides. A related pseudogene is approximately 12 kb downstream of this gene on chromosome 1. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2010],GBA,GBA1,GCB,GLUC,Cancer,Cell Type Marker,Cell Type Marker_Oligodendrocyte marker,Endocrine & Metabolism,Lipid Metabolism,Neurodegenerative Diseases,Neurodegenerative Diseases_Dopamine Signaling in Parkinsons Disease,Neuroscience,Signal Transduction,GBA

Poids moléculaire: 60kDa

ID gène: 2629

UniProt: P04062

Pathways: Cellular Glucan Metabolic Process