PCCA anticorps (Middle Region)

N° du produit ABIN954025

Détail du produit anti-PCCA anticorps

Antigène: PCCA (Propionyl CoA Carboxylase, alpha Polypeptide (PCCA))

Épitope: AA 336-365, Middle Region

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp PCCA est non-conjugé

Application: Western Blotting (WB), Enzyme Immunoassay (EIA)

Specificité: This antibody reacts to PCCA.

Réactivité croisée (Details): Species reactivity (tested):Human.

Purification: Affinity chromatography on Protein A

Immunogène: KLH conjugated synthetic peptide between 336-365 amino acids from the Central region of human PCCA

Isotype: Ig Fraction

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.25 mg/mL

Buffer: PBS, 0.09 % (W/V) sodium azide

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeated freezing and thawing.

Stock: 4 °C/-20 °C

Stockage commentaire: Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.

Détails sur PCCA

Antigène: PCCA (Propionyl CoA Carboxylase, alpha Polypeptide (PCCA))

Autre désignation: PCCA (PCCA Produits)

Synonymes: anticorps pcca, anticorps zgc:66359, anticorps C79630, anticorps wu:fb92g02, anticorps zgc:100925, anticorps propionyl-CoA carboxylase alpha subunit, anticorps propionyl-COA carboxylase alpha chain, mitochondrial, anticorps propionyl-CoA carboxylase alpha chain, anticorps zinc finger CCCH-type containing 13, anticorps propionyl-Coenzyme A carboxylase, alpha polypeptide, anticorps propionyl CoA carboxylase, alpha polypeptide, anticorps propionyl-CoA carboxylase alpha subunit L homeolog, anticorps PCCA, anticorps Pcca, anticorps BMEI0800, anticorps pccA, anticorps NRI_0781, anticorps zc3h13, anticorps pcca, anticorps pcca.L

Sujet: The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.Synonyms: PCCase subunit alpha, Propanoyl-CoA:carbon dioxide ligase subunit alpha, Propionyl-CoA carboxylase alpha chain mitochondrial

Poids moléculaire: 80059 Da

ID gène: 5095

NCBI Accession: NP_000273

Pathways: Monocarboxylic Acid Catabolic Process