PCCA anticorps

N° du produit ABIN2458000

Détail du produit anti-PCCA anticorps

Antigène: PCCA (Propionyl CoA Carboxylase, alpha Polypeptide (PCCA))

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp PCCA est non-conjugé

Application: Western Blotting (WB), ELISA

Purification: Antibody is purified by peptide affinity chromatography method.

Immunogène: Antibody produced in rabbits immunized with a synthetic peptide corresponding a region of human PCCA.

Information d'application

Indications d'application: PCCA antibody can be used for detection of PCCA by ELISA at 1:312500. PCCA antibody can be used for detection of PCCA by western blot at 1 μg/mL, and HRP conjugated secondary antibody should be diluted 1:50,000 - 100,000.

Restrictions: For Research Use only

Stockage

Format: Lyophilized

Reconstitution: Add 50 ?L of distilled water. Final antibody concentration is 1 mg/mL.

Concentration: 1 mg/mL

Buffer: Antibody is lyophilized in PBS buffer with 2 % sucrose.

Conseil sur la manipulation: As with any antibody avoid repeat freeze-thaw cycles.

Stock: 4 °C/-20 °C

Stockage commentaire: For short periods of storage (days) store at 4 °C. For longer periods of storage, store PCCA antibody at -20 °C.

Détails sur PCCA

Antigène: PCCA (Propionyl CoA Carboxylase, alpha Polypeptide (PCCA))

Autre désignation: PCCA (PCCA Produits)

Synonymes: anticorps pcca, anticorps zgc:66359, anticorps C79630, anticorps wu:fb92g02, anticorps zgc:100925, anticorps propionyl-CoA carboxylase alpha subunit, anticorps propionyl-COA carboxylase alpha chain, mitochondrial, anticorps propionyl-CoA carboxylase alpha chain, anticorps zinc finger CCCH-type containing 13, anticorps propionyl-Coenzyme A carboxylase, alpha polypeptide, anticorps propionyl CoA carboxylase, alpha polypeptide, anticorps propionyl-CoA carboxylase alpha subunit L homeolog, anticorps PCCA, anticorps Pcca, anticorps BMEI0800, anticorps pccA, anticorps NRI_0781, anticorps zc3h13, anticorps pcca, anticorps pcca.L

Sujet: PCCA is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA is the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia.The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Two transcript variants encoding different isoforms have been found for this gene.

Poids moléculaire: 75 kDa

ID gène: 5095

NCBI Accession: NP_000273

UniProt: Q8WXQ7

Pathways: Monocarboxylic Acid Catabolic Process